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Volker Straub Selected Research
Volker Straub Research Topics
Disease
54
Duchenne Muscular Dystrophy (Muscular Dystrophy, Becker)
03/2024 - 07/2002
38
Muscular Dystrophies (Muscular Dystrophy)
02/2024 - 03/2002
36
Muscular Diseases (Myopathy)
05/2024 - 10/2002
21
Limb-Girdle Muscular Dystrophies (Limb-Girdle Muscular Dystrophy)
11/2022 - 11/2004
16
Muscle Weakness
02/2024 - 08/2007
12
Disease Progression
08/2023 - 01/2013
10
Glycogen Storage Disease Type II (Pompe's Disease)
05/2022 - 07/2013
9
Rare Diseases (Rare Disease)
11/2023 - 01/2013
9
Cardiomyopathies (Cardiomyopathy)
12/2019 - 05/2009
7
Fibrosis (Cirrhosis)
01/2023 - 05/2009
6
Inborn Genetic Diseases (Disease, Hereditary)
03/2024 - 01/2008
6
Dysferlinopathy
01/2023 - 12/2005
5
type 2B Limb-girdle muscular dystrophy
11/2022 - 06/2007
5
Sarcoglycanopathies
01/2022 - 12/2008
5
Bethlem myopathy
01/2020 - 12/2013
4
Respiratory Insufficiency (Respiratory Failure)
12/2023 - 03/2014
4
Scleroatonic muscular dystrophy
01/2020 - 01/2013
4
Limb-girdle muscular dystrophy type 2A
01/2020 - 12/2007
4
Type 2I Limb-Girdle Muscular Dystrophy
01/2020 - 01/2005
4
Neuromuscular Diseases (Neuromuscular Disease)
01/2020 - 11/2013
4
Distal Myopathies (Distal Muscular Dystrophy)
11/2017 - 07/2008
4
Miyoshi myopathy
09/2010 - 03/2007
3
Muscle Hypotonia (Hypotonia)
10/2021 - 02/2012
3
Walker-Warburg Syndrome
01/2020 - 03/2002
3
Scoliosis
01/2017 - 02/2012
3
Limb-girdle muscular dystrophy type 2F
01/2013 - 12/2008
3
Ophthalmoplegia (External Ophthalmoplegia)
09/2011 - 08/2007
2
Facies
02/2024 - 10/2021
2
Proteostasis Deficiencies
10/2023 - 01/2020
2
Motor Neuron Disease (Primary Lateral Sclerosis)
10/2023 - 07/2021
2
Frontotemporal Dementia (Semantic Dementia)
10/2023 - 01/2022
2
Inflammation (Inflammations)
09/2023 - 01/2021
2
Vacuolar myopathy
01/2023 - 07/2013
2
Dyslipidemias (Dyslipidemia)
11/2022 - 07/2020
2
Muscular Atrophy (Muscle Atrophy)
11/2022 - 01/2011
2
Amyotrophic Lateral Sclerosis (Lou Gehrig's Disease)
01/2022 - 07/2021
2
Osteoporosis
01/2022 - 01/2021
2
Spinal Muscular Atrophy (Progressive Muscular Atrophy)
10/2021 - 11/2020
2
Left Ventricular Dysfunction
01/2021 - 05/2009
2
Camptocormia
01/2021 - 06/2013
2
Intellectual Disability (Idiocy)
11/2020 - 03/2017
2
Cataract (Cataracts)
05/2017 - 03/2017
2
Dilated Cardiomyopathy (Cardiomyopathy, Congestive)
07/2014 - 09/2009
2
Myasthenia Gravis
04/2014 - 03/2011
2
Myofibrillar Myopathy
03/2014 - 05/2009
2
Hereditary Myopathy with Early Respiratory Failure
03/2014 - 06/2012
2
Ehlers-Danlos Syndrome (Syndrome, Ehlers-Danlos)
09/2013 - 02/2012
2
Malignant Hyperthermia
06/2013 - 08/2007
2
1 Rippling muscle disease
03/2011 - 07/2008
Drug/Important Bio-Agent (IBA)
32
Proteins (Proteins, Gene)
FDA Link
03/2024 - 11/2004
24
Dystrophin
IBA
01/2023 - 05/2009
14
Biomarkers (Surrogate Marker)
IBA
03/2024 - 01/2013
13
Creatine Kinase (Creatine Phosphokinase)
IBA
12/2023 - 01/2005
11
Dysferlin
IBA
12/2022 - 12/2005
9
Sarcoglycans (beta Sarcoglycan)
IBA
08/2023 - 12/2008
9
Collagen
IBA
01/2021 - 11/2009
8
Glucocorticoids
IBA
03/2024 - 01/2016
8
Adrenal Cortex Hormones (Corticosteroids)
IBA
01/2022 - 11/2009
8
Dystroglycans (Dystroglycan)
IBA
01/2018 - 03/2002
6
Connectin
IBA
03/2024 - 06/2012
6
Glucosidases
IBA
05/2022 - 07/2013
6
Ryanodine Receptor Calcium Release Channel (Ryanodine Receptor)
IBA
06/2013 - 06/2002
5
Antisense Oligonucleotides
IBA
01/2023 - 01/2014
5
Acids
IBA
05/2022 - 07/2016
5
Glycogen
IBA
05/2022 - 01/2016
5
Antibodies
IBA
11/2021 - 12/2007
5
Calcium
IBA
01/2020 - 08/2007
4
protein O-mannose beta-1,2-N-acetylglucosaminyltransferase
IBA
05/2024 - 03/2002
4
Enzymes
IBA
01/2023 - 01/2021
4
human GAA protein (Myozyme)
FDA Link
12/2021 - 01/2015
4
Steroids
IBA
01/2021 - 05/2009
4
Calpain
IBA
01/2020 - 12/2007
3
Prednisone (Sone)
FDA Link
Generic
03/2024 - 01/2022
3
RNA (Ribonucleic Acid)
IBA
02/2024 - 04/2016
3
Testosterone (Sustanon)
FDA Link
09/2023 - 12/2015
3
Myostatin
IBA
01/2023 - 05/2008
3
golodirsen
IBA
01/2022 - 01/2020
3
Morpholinos
IBA
01/2021 - 10/2009
3
MicroRNAs (MicroRNA)
IBA
11/2020 - 01/2013
3
eteplirsen
IBA
10/2012 - 10/2009
2
VBP15 compound
IBA
03/2024 - 10/2022
2
Muscle Proteins (Muscle Protein)
IBA
03/2024 - 03/2011
2
Elements
IBA
11/2023 - 10/2023
2
Valosin Containing Protein
IBA
10/2023 - 01/2020
2
deflazacort
IBA
01/2022 - 01/2020
2
EP3533
IBA
01/2021 - 01/2019
2
Contrast Media
IBA
01/2021 - 12/2004
2
Troponin I
IBA
01/2021 - 09/2015
2
Malate Dehydrogenase (Dehydrogenase, Malate)
IBA
01/2020 - 07/2014
2
2,2,2',4'-tetrachloroacetophenone
IBA
01/2020 - 04/2015
2
Phosphotransferases (Kinase)
IBA
01/2017 - 03/2014
2
Myosin Light Chains (Myosin Essential Light Chain)
IBA
09/2015 - 07/2014
2
Fibronectins (Fibronectin)
IBA
04/2014 - 03/2014
2
Calcium Channels (Calcium Channel)
IBA
01/2013 - 01/2011
2
Metoprolol (Toprol-XL)
FDA Link
Generic
01/2013 - 11/2010
2
Nitric Oxide Synthase Type I (Neuronal Nitric Oxide Synthase)
IBA
12/2011 - 07/2002
2
Caveolin 3
IBA
03/2011 - 07/2008
Therapy/Procedure
26
Therapeutics
11/2022 - 11/2010
4
Enzyme Replacement Therapy
05/2022 - 07/2013
2
Noninvasive Ventilation
05/2017 - 12/2013